A 10-year old boy recently joined a soccer team and complains of muscle pain and lightheadedness after each of his last three games. Further testing identifies that he has a defect in his lipolysis pathway, specifically a mutation in the lipase that is phosphorylated in response

Q1. Many of the components for lipid synthesis need to be "activated", which happens by a variety of mechanisms. For each of the following activation processes, state WHAT is added and WHAT ENZYME catalyzes the reaction. Acetyl-CoA activation for fatty acid synthesis: WHAT is added: ENZYME: Glycerol activation for Phosphatidic Acid (PA) synthesis: WHAT is added: ENZYME: Fatty acid activation for Diacylglycerol (DAG) synthesis: WHAT is added: ENZYME: DAG activation for Phosphatidylinositol (PI) synthesis: WHAT is added: ENZYME: Choline activation for Phosphatidylcholine (PC) synthesis WHAT is added: ENZYME:

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Help Center? Question 9 Three kinds of ketone bodies are produced in the liver. All of these ketone bodies are used as source of enerery except? Selected Answer: betahydrosyacetase Correct Answer: Evaluation Method Exact Match Selected Answer: False Answers: Question 10 When the ketone bodies reach the brian they are converted back to acetyl-CoA. For this process, succinyl-CoA is the source of CoA. Question 11 False Bonus-1: Correct Answer acetone ķ If the carbonyl carbon of a C-12 fatty acyl CoA molecule is radiolabeled with C14 isotope, a minimum of how many round(s) of B-oxidatic is(are) required to produce a radioactively labeled acetyl CoA? Selected Answer: 2 Correct Answer: Evaluation Method Exact Match Case Sensitivity Correct Answer one Case Sensitivity

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104. A 32-year-old man is brought to the emergency department by ambulance 30 minutes after he was found unresponsive by his wife. Paramedics say that his blood glucose concentration was 22 mg/dL by fingerstick at the scene. He became responsive following administration of an ampule of 50% dextrose. On arrival, he says that he has a 3-month history of episodes of sweating and feeling shaky. His symptoms resolve when he eats a candy bar. Physical examination shows no abnormalities. The tentative diagnosis of insulinoma is made. In addition to a decreased glucose concentration, which of the following sets of findings in this patient during a fasting-induced hypoglycemic episode is most likely to confirm the diagnosis? A) B) C) D) E) F) Serum C Peptide ↑ Insulin 1 ↓ Urine Ketones present absent present absent present absent