Type VI glycogen storage disease (Hers disease) is a rare metabolic disorder caused by lack of phosphorylase kinase in the liver.   In your own words describe how each of the following metabolic parameters/observations will be affected/unaffected in a person with Type VI GSD (a) Blood glucose levels, after fasting (e.g. before breakfast). (b) Blood glucose levels, immediately following a meal. (c) Storage of glycogen in the liver and muscles. (d) ATP concentration in the muscles

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Nitrogen metabolism

Nitrogen metabolism is the synthesis, utilization or uptake, breakdown, and excretion of nitrogenous compounds in the body. The nitrogen metabolism encompasses nitrogen fixation, biosynthesis, and the breakdown of amino acids, purines, and pyrimidine. Since nitrogen-containing compounds are required for various life processes, nitrogen is an important element of life.