Question 15 Glycogen storage disease type I (GSD I) or von Gierke's disease, is the most common of the glycogen storage diseases. This genetic disease results from deficiency of the enzyme glucose-6-phosphatase. The metabolic outcomes of GSD I are likely to include: O Low blood glucose, increased blood pH, increased glycogen storage in liver and kidneys O High blood glucose, decreased blood pH, decreased glycogen storage in liver and kidneys O Low blood glucose, increased blood pH, decreased glycogen storage in liver and kidneys O Low blood glucose, decreased blood pH, decreased glycogen storage in liver and kidneys High blood glucose, decreased blood pH, increased glycogen storage in liver and kidneys O High blood glucose, increased blood pH, increased glycogen storage in liver and kidneys O High blood glucose, increased blood pH, decreased glycogen storage in liver and kidneys O Low blood glucose, decreased blood pH, increased glycogen storage in liver and kidneys

Introduction to General, Organic and Biochemistry
11th Edition
ISBN:9781285869759
Author:Frederick A. Bettelheim, William H. Brown, Mary K. Campbell, Shawn O. Farrell, Omar Torres
Publisher:Frederick A. Bettelheim, William H. Brown, Mary K. Campbell, Shawn O. Farrell, Omar Torres
Chapter30: Nutrition
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Question 15
Glycogen storage disease type I (GSD I) or von Gierke's disease, is the most common of the glycogen
storage diseases. This genetic disease results from deficiency of the enzyme glucose-6-phosphatase.
The metabolic outcomes of GSD I are likely to include:
O Low blood glucose, increased blood pH, increased glycogen storage in liver and kidneys
O High blood glucose, decreased blood pH, decreased glycogen storage in liver and kidneys
O Low blood glucose, increased blood pH, decreased glycogen storage in liver and kidneys
O Low blood glucose, decreased blood pH, decreased glycogen storage in liver and kidneys
High blood glucose, decreased blood pH, increased glycogen storage in liver and kidneys
O High blood glucose, increased blood pH, increased glycogen storage in liver and kidneys
O High blood glucose, increased blood pH, decreased glycogen storage in liver and kidneys
O Low blood glucose, decreased blood pH, increased glycogen storage in liver and kidneys
Transcribed Image Text:Question 15 Glycogen storage disease type I (GSD I) or von Gierke's disease, is the most common of the glycogen storage diseases. This genetic disease results from deficiency of the enzyme glucose-6-phosphatase. The metabolic outcomes of GSD I are likely to include: O Low blood glucose, increased blood pH, increased glycogen storage in liver and kidneys O High blood glucose, decreased blood pH, decreased glycogen storage in liver and kidneys O Low blood glucose, increased blood pH, decreased glycogen storage in liver and kidneys O Low blood glucose, decreased blood pH, decreased glycogen storage in liver and kidneys High blood glucose, decreased blood pH, increased glycogen storage in liver and kidneys O High blood glucose, increased blood pH, increased glycogen storage in liver and kidneys O High blood glucose, increased blood pH, decreased glycogen storage in liver and kidneys O Low blood glucose, decreased blood pH, increased glycogen storage in liver and kidneys
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